Oxycephalic child with mild clinical aspects of Crouzon syndrome that has been operated elsewhere twice. Primarily a median craniectomy had been performed. Reossification failed to appear and a pronounced turricephalic head shape developed. Years later another team tried to cover the extensive bone defect with PMMA, which subsequently broke. At first referral in our craniofacial unit skull radiographs demonstrated an extreme brachy- and turricephalic head with multiple pieces of PMMA as well as signs of elevated ICP. Our opertive approach was a fronto-orbital advancement and cranial remodelling to achieve more intracranial space and reduce the turricephalic aspect. Intraopertively we were not able to sufficiently reduce the height. Therefore after removing all PMMA we broadened the skull. With an individual orthotic device over the next monrths we managed to achieve a significant improvement. Although we do see some reossification a further opertice approach is in order to cover the bony defect.

Part of Session

CRANIOFACIAL